Intracranial venous sinus thrombosis（ CVST） is a cerebrovascular disease caused by cerebral venous and cerebrospinal fluid malabsorption disorder caused by venous sinus thrombosis. The etiology of CVST is complicated， and nephrotic syndrome（ NS） is considered to be one of the important causes of CVST. At present， there are increasingly cases and studies on NS combined with CVST in China and abroad. Therefore， this article reviews the pathogenesis， diagnosis， treatment and related research progress of adult NS combined with CVST in order to improve clinicians' understanding of NS combined with CVST.